en شنوایی شناسی Audiology گزارش موردي Case Reports Two sibling cases with a temperature-sensitive form of auditory neuropathy from a consanguineous marriage of Iranian descent have been described. They complained about the temporary loss of hearing and compromised speech comprehension after a slight fever or elevating the body temperature by vigorous exercises. A series of tests including brain MRI, pure-tone audiometry, speech audiometry in quiet and noise, tympanometry, reflexometry, TEOAEs, cochlear microphonic, and ABR were performed in a 24-hours interval at both febrile and afebrile states, and results are reported here. This report is the first example of temperature-sensitive auditory neuropathy in this geographical region. Auditory neuropathy, Temperature-sensitive, Case reports, Consanguineous marriage 337 342 http://irj.uswr.ac.ir/browse.php?a_code=A-10-1411-1&slc_lang=en&sid=1 Nasrin Yazdani nasrin_yazdani2000@yahoo.com 0000-0003-1006-289x No Department of Otorhinolaryngology, Otorhinolaryngology Research Center, Amir-Alam Hospital, Tehran University of Medical Sciences, Tehran, Iran. Mohsen Ahadi mohsenahadi@gmail.com 0000-0002-8591-2361 Yes Department of Audiology, Rehabilitation Research Center, School of Rehabilitation Sciences, Iran University of Medical Sciences, Tehran, Iran.